产品详情
  • 产品名称:Anti-IDUA抗体

  • 产品型号:α-L-艾杜糖苷酶抗体
  • 产品厂商:KALANG
  • 产品文档:
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简单介绍:
Anti-IDUA抗体产品质量稳定,实验效果明显,货期快,价格优惠,欢迎垂询订购!我公司长期供应**组化抗体、WB抗体、**组化试剂盒和抗体试验所需全部相关试剂、荧光标记抗体、单克隆抗体、多克隆抗体、各种标记的二抗IgG/IgM/IgD/IgA等科研实验抗体。Anti-IDUA抗体用于**组化实验,WB实验,相应的标记抗体有HRP标记抗体,FITC标记,BIO等。
详情介绍:
Rabbit Anti-IDUA
Cat. Number:
Anti-IDUA抗体KL-15542R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan Anti-IDUA抗体sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008].
Also known as:
IDUA_HUMAN; Alpha-L-iduronidase; Anti-IDUA抗体IDA; Iduronidase alpha L; MPS1.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Horse, .
Immunogen: KLH conjugated synthetic peptide derived from human IDUA.
Predicted Molecular Weight: 70kDa. Anti-IDUA抗体
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications. Anti-IDUA抗体
Optimal working dilutions must be determined by the end user.
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