产品详情
简单介绍:
Anti-ETHE1抗体产品质量稳定,实验效果明显,货期快,价格优惠,欢迎垂询订购!我公司长期供应**组化抗体、WB抗体、**组化试剂盒和抗体试验所需全部相关试剂、荧光标记抗体、单克隆抗体、多克隆抗体、各种标记的二抗IgG/IgM/IgD/IgA等科研实验抗体。Anti-ETHE1抗体用于**组化实验,WB实验,相应的标记抗体有HRP标记抗体,FITC标记,BIO等。
详情介绍:
Rabbit Anti-ETHE1
Cat. Number:
Anti-ETHE1抗体KL-7610R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Probably plays an important role in metabolic homeostasis in mitochondria. May function as a nuclear-cytoplasmic shuttling
Anti-ETHE1抗体protein that binds transcription factor RELA/NFKB3 in the nucleus and exports it to the cytoplasm. Suppresses p53-induced apoptosis by preventing nuclear localization of RELA.
Involvement in disease:Defects in ETHE1 are a cause of ethylmalonic encephalopathy (EE) . EE is an autosomal recessive disorder characterized by neurodevelopmental delay and regression, recurrent petechiae, acrocyanosis, Anti-ETHE1抗体diarrhea, leading to death in the first decade of life. It is also associated with persistent lactic acidemia and ethylmalonic and methylsuccinic aciduria.
Involvement in disease:Defects in ETHE1 are a cause of ethylmalonic encephalopathy (EE) . EE is an autosomal recessive disorder characterized by neurodevelopmental delay and regression, recurrent petechiae, acrocyanosis, Anti-ETHE1抗体diarrhea, leading to death in the first decade of life. It is also associated with persistent lactic acidemia and ethylmalonic and methylsuccinic aciduria.
Also known as:
mitochondrial; Ethe1; ETHE1
Anti-ETHE1抗体protein, mitochondrial precursor; ETHE1_HUMAN; ethylmalonic encephalopathy 1; Ethylmalonic encephalopathy protein 1; hepatoma subtracted clone one; Hepatoma subtracted clone one protein; HSCO; Protein ETHE1; YF13H12.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Dog, Pig, Cow, Rabbit, Sheep, .
●
Immunogen: KLH conjugated synthetic peptide derived from human ETHE1.
●
Predicted Molecular Weight: 26kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications. Anti-ETHE1抗体
Optimal working dilutions must be determined by the end user.
Not yet tested in other applications. Anti-ETHE1抗体
Optimal working dilutions must be determined by the end user.
kl215Mu01 中心体肌动蛋白β(CTRN2)多克隆抗体 Polyclonal Antibody to Centractin Beta (CTRN2)
kl215Ra01 中心体肌动蛋白β(CTRN2)多克隆抗体 Polyclonal Antibody to Centractin Beta (CTRN2)
kl297Hu01 核糖核酸酶A(RNASE1)多克隆抗体 Polyclonal Antibody to Ribonuclease A (RNASE1)
kl762Hu01 磷酸化酶激酶β(PHKβ)多克隆抗体 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl762Mu01 磷酸化酶激酶β(PHKβ)多克隆抗体 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl762Ra01 磷酸化酶激酶β(PHKβ)多克隆抗体 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl178Hu01 α2-HS糖蛋白(αHSG)多克隆抗体 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl178Mu01 α2-HS糖蛋白(αHSG)多克隆抗体 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl178Ra01 α2-HS糖蛋白(αHSG)多克隆抗体 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl545Hu01 **球蛋白E(IgE)多克隆抗体 Polyclonal Antibody to Immunoglobulin E (IgE)
kl545Mu01 **球蛋白E(IgE)多克隆抗体 Polyclonal Antibody to Immunoglobulin E (IgE)
kl545Ra01 **球蛋白E(IgE)多克隆抗体 Polyclonal Antibody to Immunoglobulin E (IgE)
kl436Hu01 肌球蛋白ⅠG(MYO1G)多克隆抗体 Polyclonal Antibody to Myosin IG (MYO1G)
kl436Mu01 肌球蛋白ⅠG(MYO1G)多克隆抗体 Polyclonal Antibody to Myosin IG (MYO1G)
kl436Ra01 肌球蛋白ⅠG(MYO1G)多克隆抗体 Polyclonal Antibody to Myosin IG (MYO1G)
kl435Hu01 肌球蛋白ⅠF(MYO1F)多克隆抗体 Polyclonal Antibody to Myosin IF (MYO1F)
kl435Mu01 肌球蛋白ⅠF(MYO1F)多克隆抗体 Polyclonal Antibody to Myosin IF (MYO1F)
kl435Ra01 肌球蛋白ⅠF(MYO1F)多克隆抗体 Polyclonal Antibody to Myosin IF (MYO1F)