产品详情
简单介绍：
Anti-DKC1抗体产品质量稳定，实验效果明显，货期快，价格优惠，欢迎垂询订购！我公司长期供应**组化抗体、WB抗体、**组化试剂盒和抗体试验所需全部相关试剂、荧光标记抗体、单克隆抗体、多克隆抗体、各种标记的二抗IgG/IgM/IgD/IgA等科研实验抗体。Anti-DKC1抗体用于**组化实验,WB实验,相应的标记抗体有HRP标记抗体,FITC标记,BIO等。
详情介绍：
Rabbit Anti-DKC1
Cat. Number:
Anti-DKC1抗体KL-13007R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Dyskerin (NAP57) associates
Anti-DKC1抗体with the chaperone protein Nopp140 and forms a small ribonucleoprotein particle with GAR1 (NOLA1), NHP2 (NOLA2) and Nop10 for the isomerization of uridine to pseudouridine (1). GAR1, NHP2 and dyskerin localize to the dense fibrillar component of the nucleolus and in nuclear Cajal bodies (2). The dyskerin gene maps to chromosome Xq28 (3). Missense mutations in the dyskerin gene interfere with normal nuclear localization of dyskerin and cause Dyskeratosis congenita (DKC) (4). DKC is a rare, X-linked bone marrow disorder characterized by cutaneous hyperpigmentation, dystrophy of the nails, atrophy of the testicles and leukoplakia of the oral mucosa. The GAR1 gene maps to chromosome 4q25 (5,6). The NHP2 gene maps to chromosome 5q35.3 and encodes a 155-amino acid protein (2,7).
Also known as:
CBF5; CBF5 homolog;
Anti-DKC1抗体Cbf5p homolog; DKC 1; DKC; Dkc1; DKC1_HUMAN; DKCX; Dyskeratosis congenita 1; Dyskeratosis congenita 1 dyskerin; Dyskerin; H/ACA ribonucleoprotein complex subunit 4; NAP 57; NAP57; NAP-57; NOLA 4; NOLA4; Nopp140 associated protein of 57 kDa; Nopp140-associated protein of 57 kDa; Nucleolar protein family A member 4; Nucleolar protein NAP57; snoRNP protein DKC1; XAP 101; XAP101.
Specificity:
●
Rabbit Polyclonal IgG,
Anti-DKC1抗体affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
●
Immunogen: KLH conjugated synthetic peptide derived from human DKC1/Dys.
●
Predicted Molecular Weight: 58kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Anti-DKC1抗体
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl243Hu01 拓扑异构酶Ⅰ(TOP1)多克隆抗体 Polyclonal Antibody to Topoisomerase I (TOP1)
kl246Mu01 磷酸肌醇依赖性蛋白激酶1(PDPK1)多克隆抗体 Polyclonal Antibody to Phosphoinositide Dependent Protein Kinase 1 (PDPK1)
kl257Hu01 62kDa核孔蛋白(NUP62)多克隆抗体 Polyclonal Antibody to Nucleoporin 62kDa (NUP62)
kl260Hu01 融合蛋白(FUS)多克隆抗体 Polyclonal Antibody to Fusion (FUS)
kl260Mu01 融合蛋白(FUS)多克隆抗体 Polyclonal Antibody to Fusion (FUS)
kl262Hu01 紧密连接蛋白1(TJP1)多克隆抗体 Polyclonal Antibody to Tight Junction Protein 1 (TJP1)
kl268Hu01 11-β-羟基类固醇脱氢酶1(HSD11β1)多克隆抗体 Polyclonal Antibody to 11-Beta-Hydroxysteroid Dehydrogenase Type 1 (HSD11b1)
kl268Ra01 11-β-羟基类固醇脱氢酶1(HSD11β1)多克隆抗体 Polyclonal Antibody to 11-Beta-Hydroxysteroid Dehydrogenase Type 1 (HSD11b1)
kl270Hu01 7-脱氢胆固醇还原酶(DHCR7)多克隆抗体 Polyclonal Antibody to 7-Dehydrocholesterol Reductase (DHCR7)
kl276Hu01 氨基酰化酶1(ACY1)多克隆抗体 Polyclonal Antibody to Aminoacylase 1 (ACY1)
kl281Hu01 腺苷激酶(ADK)多克隆抗体 Polyclonal Antibody to Adenosine Kinase (ADK)
kl284Hu01 α白蛋白(AFM)多克隆抗体 Polyclonal Antibody to Afamin (AFM)
kl284Mu01 α白蛋白(AFM)多克隆抗体 Polyclonal Antibody to Afamin (AFM)
kl285Hu01 前梯度蛋白2(AGR2)多克隆抗体 Polyclonal Antibody to Anterior Gradient Protein 2 (AGR2)
kl288Hu01 同种异体移植炎症因子1(AIF1)多克隆抗体 Polyclonal Antibody to Allograft Inflammatory Factor 1 (AIF1)
kl288Mu01 同种异体移植炎症因子1(AIF1)多克隆抗体 Polyclonal Antibody to Allograft Inflammatory Factor 1 (AIF1)
